Vol. 1, Issue 1, Part A (2019)

Dego’s disease, is a rare multisystemic vasculopathy, usually benign with involvement of cutaneous vessels, however at times can turn malignant with widespread thrombosis particularly involving vessels of gastrointestinal tract and central nervous system. In the current manuscript, we describe a rare case of Dego’s disease- the benign atrophic papulosis variant unmasking systemic thrombotic microangiopathy in a young patient of systemic lupus erythematosus.